Emerg Infect DiseidEmerging Infectious Diseases1080-60401080-6059Centers for Disease Control89692502639929Research ArticleCreutzfeldt-Jakob disease in the United States, 1979-1994: using national mortality data to assess the possible occurrence of variant cases.HolmanR. C.KhanA. S.BelayE. D.SchonbergerL. B.Centers for Disease Control and Prevention, Atlanta, Georgia, USA.Oct-Dec199624333337

After a cluster of Creutzfeldt-Jakob disease (CJD) cases among unusually young patients was reported recently from the United Kingdom, we examined trends and the current incidence of CJD in the United States. We found that the age-adjusted CJD death rate in the United States is similar to published estimates of the crude incidence of CJD worldwide and has continued to be stable from 1979 through 1994. The number of CJD deaths in persons